Desmoplastic small round cell tumors are a type of soft tissue cancer that mostly begin in the abdomen. This type of cancer is rare and mostly affects boys and young men.
These tumora can be aggressive and tend to form multiple tumors in the peritoneumand pelvis.
Desmoplastic small round cell tumors can rapidly spread to other organs of the abdominal cavity. Treatment usually involves combination treatment, such as surgery, chemotherapy and radiation therapy.